EP2004176B1 - USE of N- ( DIBENZ (b, F) OXEPIN-10-YLMETHYL ) N-METHYL-N- PROP- 2 -YNYLAMINE (OMIGAPIL) for the PROPHYLAXIS and / or TREATMENT of CONGENITAL MUSCULAR DYSTROPHY or MYOPATHY RESULTING from COLLAGEN VI DEFICIENCY